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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications with fulltext
Open Access
61 %
Mots clés
Omics
Effector T cells
GENE
Myogenesis
Gene therapy
Skeletal muscle
Neuromuscular junction NMJ
Ageing
ALS
AAV vectors
Accelerometry
DNA methylation
MUTATIONS
Anti-fibrotic pharmacotherapies
Dystrophin
PABPN1 agregates
Differentiation
BINDING SPECIFICITY
Annexin A2
Regeneration
Myotube
Calcium
FAPs
Muscular dystrophy
Andermann syndrome
Myopathies
2-D PAGE
Anti-acetylcholine receptor antibodies
Cell therapy
Regenerative medicine
Geriatric assessment
FSHD
Autoimmune diseases
AChR antibodies
Antiserum
Actin
DUX4
Biomarker
Xenograft
Haploinsufficiency
Cross-bridge kinetics
Triplet expansion disease
Antisens oligonucleotides
Neuromuscular disease
Exon-skipping
ARN
Amyotrophic Lateral Sclerosis
AUTOPHAGY
Regulatory T cells
Inflammation
Agrégats de PABPN1
Pharyngeal muscle
Alphavirus
Atrophy
Lamins
Muscle strength
Thérapie génique
Autologous
Myosin
Satellite cells
Pax7
DMD
Duchenne muscular dystrophy
Muscle fibrosis
Akt
Dystrophie musculaire oculopharyngée
Aged
Fibrosis
Sarcopenia
Aav-U7
Functional genomics
Transcriptomics
Mass spectrometry
Myoblasts
Gene replacement
Bile salt hydrolases
Dysferlinopathy
Epigenetics
Muscle stem cells
Oculopharyngeal muscular dystrophy
APOPTOSIS
AAV
Arbovirus
Adipose tissue
Muscle
Satellite cell
Metabolism
Myoblast
Myositis
OPMD
Nuclear envelope
Muscle dystrophy
Alzheimer's disease
Human
Dysferlin
Myopathy
PABPN1
RNA
Aggregate
Intercellular communication